Suzi Demirbag
Gulhane Military Medical Academy, Tukey
Title: Hirschsprung associated enterocolitis: A deadly complication of Hirschsprung’s Disease
Biography
Biography: Suzi Demirbag
Abstract
Hirschsprung’s disease (HD) was first described by Herald Hirschsprung in 1886. HD is one of the most important cause of the constipation in childhood. It occurs one in 5000 live birth and male/female ratio is around four. Failure to diagnose the problem may cause morbidity and sometimes mortality. Hirschsprung associated enterocolitis (HAEC) is a severe results of the disease and responsible for 50% mortality associated with HD. HAEC is a potentially deadly complication of HD and characterized by fever, abdominal distention, vomiting, diarrhea, sepsis and if not treated appropriately may result with mortality. Despite a lot of clinical and experimentally studies, the exact mechanisms underlying HAEC are still unclear. This presentation mainly focuses on risk factors, early diagnosis and current treatment protocols for HAEC.