6th World Pediatric Congress

Biography

Biography: Tania Martins

Abstract

Introduction: Congenital pulmonary malformations (CPM) are rare with an incidence of 30-42/100,000. Clinical presentation varies from asymptomatic with late diagnosis, until early and severe clinical manifestation, requiring early surgical intervention. Aim: Aim of this study is to determine the incidence, prenatal diagnosis, complementary means of diagnosis and treatment.
Methods: Method used in this study is a retrospective review in a neonatal intensive care unit in a Tertiary Hospital between 2001 and 2015.
Results: 24 cases were identified in which there were 11 cystic adenomatoid malformations (45.8%), 7F/4M. Prenatal diagnosis was found in 100% of cases with mean gestational age 23s, right 54.5%. Prenatal diagnosis in 2 cases was not confirmed postnatally, two with later diagnosis of esophageal atresia and lymphangioma and 1 awaits confirmation. Symptomatic at birth and with associated malformations were 18.2%. All patients underwent computed tomography (CT) chest that corroborated the diagnosis in 72.7%. Undergoing surgery were 72.7% (63.6% lobectomy). Nine (37.5%) pulmonary sequestration: 7 extra-lobar (4 left / 3 right) and two intra-lobar (1 left/1 right), 6M/3F. Prenatal diagnosis was done in 88.9% and correct in 25%. Symptomatic at birth were 22.2%. Associated malformations were in 44.4%. Within the extra sequestration lobar 55.5% underwent surgical excision and 100% of intra-lobar embolization of vessels by catheterization. Four pulmonary emphysema were identified (16.6%), 3M/1F. Without prenatal diagnosis, asymptomatic at birth and right location were seen in 100%. Malformations associated at 75%. All underwent lobectomy by thoracotomy. Conclusions: In recent years, improve in general orientation of CPM due to prenatal and postnatal diagnosis is more accurate, allows the early establishment of an appropriate therapeutic guidance.